How holistic nursing can enhance the quality of life of children with cystic fibrosis.

Tointon, K. and Hunt, J. A., 2016. How holistic nursing can enhance the quality of life of children with cystic fibrosis. Nursing Children and Young People, 28 (8), 22 - 25.

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DOI: 10.7748/ncyp.2016.e753


Cystic fibrosis is one of the most common life limiting autosomal recessive genetically inherited conditions affecting Caucasians. It is caused by mutations of chromosome 7 responsible for encoding amino acid protein 1480, the cystic fibrosis transmembrane conductance regulator (CFTR) protein. The most common mutation, affecting 75% of patients with CF in the UK, is that of delta F508 which results in the omission of phenylalanine at position 508 in the 1480 chain. However, other rarer mutations exist resulting in differing presentations of the condition. Ellen, a teenager with a rarer presentation of CF, and her family, are drawn upon in this case study to discuss living with CF and its impact upon quality of life and well-being in life limiting conditions of childhood.

Item Type:Article
Uncontrolled Keywords:child health ; cystic fibrosis ; lif-limiting illness ; paediatrics ; respiratory system ; well-being
Group:Faculty of Health & Social Sciences
ID Code:26516
Deposited By: Unnamed user with email symplectic@symplectic
Deposited On:23 Jan 2017 16:50
Last Modified:26 Jul 2017 15:10


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